mitocondria Tag

Glutaric aciduria I: creatine supplementation restores creatinephosphate levels in mixed cortex cells from rat incubated with 3-hydroxyglutarate 2003

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27 diciembre, 2024 / 0 Comments

P-201 Mild disruption of bioenergetics associated with marked histological alterations in striatum of glutaryl-CoA dehydrogenase deficient mice submitted to a lysine overload 2004

12 octubre, 2022 / 0 Comments

P-030 COMPARTMENTALIZATION OF LYSINE METABOLISM AND ITS ROLE FOR GLUTARYL-COA DEHYDROGENASE DEFICIENCY 2011

08 octubre, 2022 / 0 Comments

Disturbance of Mitochondrial Dynamics, Endoplasmic Reticulum–Mitochondria Crosstalk, Redox Homeostasis, and Inflammatory Response in the Brain of Glutaryl-CoA Dehydrogenase-Deficient Mice: Neuroprotective Effects of Bezafibrate 2022

20 julio, 2022 / 0 Comments

Organic acidurias: Major gaps, new challenges, and a yet unfulfilled promise 2021

30 diciembre, 2021 / 0 Comments

The lysine degradation pathway: Subcellular compartmentalization and enzyme deficiencies 2020

09 enero, 2021 / 0 Comments

Glutaric aciduria I creatine supplementation restores creatinephosphate levels in mixed cortex cells from rat incubated with 3-hydroxyglutarate 2003

26 octubre, 2020 / 0 Comments

The lysine degradation pathway Subcellular compartmentalization and enzyme deficiencies 2020

14 septiembre, 2020 / 0 Comments

Organic acidurias Major gaps, new challenges, and a yet unfulfilled promise 2020

14 septiembre, 2020 / 0 Comments

Disease-Linked Glutarylation Impairs Function and Interactions of Mitochondrial Proteins and Contributes to Mitochondrial Heterogeneity 2018

16 septiembre, 2019 / 0 Comments